Primary erythromelalgia: a clinical diagnosis

Primary erythromelalgia: a clinical diagnosis

Maria Sousa-Dias 1, Mariana Meneses 1, Nádia Rodrigues 1

1 Department of Pediatrics, Hospital Pedro Hispano, Matosinhos, Portugal

Maria Sousa-Dias, Mariana Meneses, Nádia Rodrigues

La información completa de afiliaciones y autor de correspondencia está disponible en la versión original en PDF.

*Correspondence: Maria Sousa-Dias, Email not available

Abstract

Erythromelalgia is a rare chronic disorder characterized by a triad of intermittently red, hot and painful extremities. The syndrome usually affects the lower extremities with symmetrical cutaneous findings, but may also involve the upper extremities and, rarely, the face and present with unilateral involvement only.

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