Systemic Juvenile Idiopathic Arthritis: A Challenging Diagnosis

  • Inês Pinto Ferreira
  • Paula Correia
  • Marta Cabral


Systemic juvenile idiopathic arthritis (SJIA) is a disease challenging to diagnose.  Its onset can be quite nonspecific, suggesting other entities. The authors present the case of a 17-year-old adolescent, with a clinical picture lasting for 5 months characterized by intermittent polyarthritis and myalgia, associated with fever and exanthema some months later. During clinical investigation, elevation of inflammatory markers was found, and infectious, oncologic and other autoimmune diseases were excluded. This patient also met criteria compatible with macrophagic activation syndrome secondary to SJIA.  This entity implies a high index of suspicion and should be early recognized by the clinician because of its implications in terms of morbidity and mortality.


Download data is not yet available.

Author Biography

Inês Pinto Ferreira

Interna do 3º ano do Departamento de Pediatria do Hospital Porf Doutor Fernando Fonseca

Case reports

Most read articles by the same author(s)

1 2 > >>