Poland syndrome: from the perspective of invasive electrophysiology in a pediatric patient – A case report

Poland syndrome: from the perspective of invasive electrophysiology in a pediatric patient – A case report

Elibet Chávez-González 1, Armando E. Hernández Castellón 1, Fernando Rodríguez-González 1, Juan M. Cruz-Elizundia 1

1 Electrophysiology Department, Cardiocentro Ernesto Guevara, Santa Clara, Cuba

Elibet Chávez-González, Armando E. Hernández Castellón, Fernando Rodríguez-González, Juan M. Cruz-Elizundia

La información completa de afiliaciones y autor de correspondencia está disponible en la versión original en PDF.

*Correspondence: Armando E. Hernández Castellón, Email not available

Abstract

Introduction: Poland syndrome is a rare congenital condition characterized by the unilateral absence or hypoplasia of the pectoralis major muscle, often with ipsilateral upper limb malformations. Cardiac displacement may complicate invasive procedures. Case report: A 15-year-old female with Poland syndrome and recurrent palpitations presented with documented atrioventricular nodal reentrant tachycardia (AVNRT). During the electrophysiological study, mesocardia altered expected catheter positions. Ablation was successfully performed under fluoroscopic guidance. Discussion: This case highlights the need to recognize anatomical variants in Poland syndrome when planning cardiac interventions. Successful ablation is feas

Keywords:  Poland syndrome. Congenital cardiac displacement. Mesocardia. Pediatric arrhythmia. Radiofrequency catheter ablation. Case report.

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